Common etiologies
In most nonsmoking adults with a normal chest x-ray who do not take ACE inhibitors, chronic cough is caused by one or more of four conditions:[2]Irwin RS, French CL, Chang AB, et al. Classification of cough as a symptom in adults and management algorithms: CHEST guideline and expert panel report. Chest. 2018 Jan;153(1):196-209.
http://journal.chestnet.org/article/S0012-3692(17)32918-5/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/29080708?tool=bestpractice.com
[3]Morice AH, Millqvist E, Bieksiene K, et al. ERS guidelines on the diagnosis and treatment of chronic cough in adults and children. Eur Respir J. 2020 Jan;55(1):1901136.
https://erj.ersjournals.com/content/55/1/1901136.long
http://www.ncbi.nlm.nih.gov/pubmed/31515408?tool=bestpractice.com
[7]Gonlugur U, Gonlugur TE. Eosinophilic bronchitis without asthma. Int Arch Allergy Immunol. 2008;147(1):1-5.
http://www.karger.com/Article/FullText/128580
http://www.ncbi.nlm.nih.gov/pubmed/18446047?tool=bestpractice.com
[8]Canning BJ, Chang AB, Bolser DC, et al. Anatomy and neurophysiology of cough: CHEST Guideline and Expert Panel report. Chest. 2014 Dec;146(6):1633-48.
https://journal.chestnet.org/article/S0012-3692(15)51535-3/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/25188530?tool=bestpractice.com
Upper airway cough syndrome (formerly postnasal drip syndrome)
Asthma
Gastroesophageal reflux disease
Nonasthmatic eosinophilic bronchitis.
More than one cause of chronic cough is often present. Truly idiopathic cough is rare and is a diagnosis of exclusion.[9]Ramanuja S, Kelkar P. Habit cough. Ann Allergy Asthma Immunol. 2009 Feb;102(2):91-5.
http://www.ncbi.nlm.nih.gov/pubmed/19230457?tool=bestpractice.com
[10]Ojoo JC, Everett CF, Mulrennan SA, et al. Management of patients with chronic cough using a clinical protocol: a prospective observational study. Cough. 2013 Jan 24;9(1):2.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC3565860
http://www.ncbi.nlm.nih.gov/pubmed/23347748?tool=bestpractice.com
Cough as a principal or sole symptom of asthma, known as cough-variant asthma, is present in a subgroup of patients. The cough may be productive and may be worse at night or with exercise. There may be absence of variable airflow limitation.[11]Global Initiative for Asthma. Global strategy for asthma management and prevention (2024 update). May 2024 [internet publication].
https://ginasthma.org/2024-report
These commonest causes account for most patients presenting to specialty clinics with chronic cough and should generally be considered first if there are no signs or symptoms pointing to alternative diagnoses.
Other common causes include the following.
ACE inhibitors: dry cough, typically associated with a tickling or scratching sensation in the throat. The reported incidence varies.[12]Bangalore S, Kumar S, Messerli FH. Angiotensin-converting enzyme inhibitor associated cough: deceptive information from the Physicians' Desk Reference. Am J Med. 2010 Nov;123(11):1016-30.
https://www.doi.org/10.1016/j.amjmed.2010.06.014
http://www.ncbi.nlm.nih.gov/pubmed/21035591?tool=bestpractice.com
ACE inhibitor-induced cough is more frequent in women than men and is associated with increasing age.[13]Alharbi FF, Kholod AAV, Souverein PC, et al. The impact of age and sex on the reporting of cough and angioedema with renin-angiotensin system inhibitors: a case/noncase study in VigiBase. Fundam Clin Pharmacol. 2017 Dec;31(6):676-84.
https://www.doi.org/10.1111/fcp.12313
http://www.ncbi.nlm.nih.gov/pubmed/28767167?tool=bestpractice.com
[14]Brugts JJ, Arima H, Remme W, et al. The incidence and clinical predictors of ACE-inhibitor induced dry cough by perindopril in 27,492 patients with vascular disease. Int J Cardiol. 2014 Oct 20;176(3):718-23.
https://www.doi.org/10.1016/j.ijcard.2014.07.108
http://www.ncbi.nlm.nih.gov/pubmed/25189490?tool=bestpractice.com
Postinfectious cough: postinfectious cough is the most common etiology of subacute cough.[6]Kwon NH, Oh MJ, Min TH, et al. Causes and clinical features of subacute cough. Chest. 2006 May;129(5):1142-7.
http://journal.chestnet.org/article/S0012-3692(15)50691-0/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/16685003?tool=bestpractice.com
A history typical for postinfectious cough should prompt watchful waiting and symptomatic therapy as necessary.
Chronic bronchitis: adult with a history of chronic productive cough lasting for more than 3 months of the year and for at least 2 consecutive years when other diagnoses have been ruled out.[15]Malesker MA, Callahan-Lyon P, Madison JM, et al. Chronic cough due to stable chronic bronchitis: CHEST Expert Panel Report. Chest. 2020 Aug;158(2):705-18.
https://journal.chestnet.org/article/S0012-3692(20)30324-X/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/32105719?tool=bestpractice.com
Chronic bronchitis is one of the manifestations of chronic obstructive pulmonary disease. Predisposing factors include nicotine and marijuana smoking, second-hand exposure to nicotine smoke, and environmental exposure to toxins.[8]Canning BJ, Chang AB, Bolser DC, et al. Anatomy and neurophysiology of cough: CHEST Guideline and Expert Panel report. Chest. 2014 Dec;146(6):1633-48.
https://journal.chestnet.org/article/S0012-3692(15)51535-3/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/25188530?tool=bestpractice.com
[16]Tarlo SM, Altman KW, Oppenheimer J, et al. Occupational and environmental contributions to chronic cough in adults: chest expert panel report. Chest. 2016 Oct;150(4):894-907.
http://www.ncbi.nlm.nih.gov/pubmed/27521735?tool=bestpractice.com
Bordetella pertussis: when local epidemiology indicates a high rate of pertussis infection, testing for Bordetella pertussis is recommended. If tests are supportive of pertussis, specific antimicrobial therapy is indicated.
Less common etiologies
Diagnoses to consider are those that impart cough through stimulation of airway mechanical and chemical receptors that feed into the vagus nerve, including afferent nerves located in the chest wall, diaphragm, esophagus, abdominal wall, and external auditory meatus.[8]Canning BJ, Chang AB, Bolser DC, et al. Anatomy and neurophysiology of cough: CHEST Guideline and Expert Panel report. Chest. 2014 Dec;146(6):1633-48.
https://journal.chestnet.org/article/S0012-3692(15)51535-3/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/25188530?tool=bestpractice.com
Other potential causes therefore are:
Disorders that distort or irritate the airway (e.g., bronchiectasis, chronic suppurative lung disease, endobronchial tumors, granulomatous disease, foreign bodies)
Disorders of lung parenchyma (e.g., interstitial lung disease resulting from hypersensitivity pneumonitis, occupational/environmental exposure, or autoimmune diseases such as systemic lupus erythematosus)
Systemic diseases (e.g., rheumatoid arthritis, sarcoidosis) or autoimmune diseases such as systemic lupus erythematosus
Chronic vagal neuropathy (e.g., vitamin B12 neuropathy, diabetic neuropathy, herpes zoster infection, chemical irritant exposure)
Irritation of the external ear canal by an infection, wax, or hearing aids may produce cough, through a reflex mediated by Arnold's nerve
Obstructive sleep apnea may cause repeated drops in intrapleural pressure, resulting in episodes of nocturnal aspiration, throat irritation and cough.[17]Sundar KM, Stark AC, Dicpinigaitis P. Chronic cough and obstructive sleep apnea. Sleep Med Clin. 2024 Jun;19(2):239-51.
http://www.ncbi.nlm.nih.gov/pubmed/38692749?tool=bestpractice.com
Oral-pharyngeal dysphagia that results in recurrent aspiration of foods and liquids may also cause cough. Patients with cough who report difficulty swallowing should be further evaluated for such etiology.
Zenker diverticulum can cause chronic cough, accompanied by dysphagia, regurgitation, aspiration, and weight loss.[18]Siddiq MA, Sood S, Strachan D. Pharyngeal pouch (Zenker's diverticulum). Postgrad Med J. 2001 Aug;77(910):506-11.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC1742115
http://www.ncbi.nlm.nih.gov/pubmed/11470929?tool=bestpractice.com
Bronchiolitis should also be considered, and may result from infection, or may be drug/toxin-related. Diffuse panbronchiolitis should be considered in patients from East Asia.[19]Azuma A, Kudoh S. Diffuse panbronchiolitis in East Asia. Respirology. 2006 May;11(3):249-61.
https://onlinelibrary.wiley.com/doi/10.1111/j.1440-1843.2006.00845.x
http://www.ncbi.nlm.nih.gov/pubmed/16635082?tool=bestpractice.com
[20]Kudoh S, Keicho N. Diffuse panbronchiolitis. Clin Chest Med. 2012 Jun;33(2):297-305.
http://www.ncbi.nlm.nih.gov/pubmed/22640847?tool=bestpractice.com
Neurologic conditions affecting the medulla oblongata or cerebellum may increase the cough reflex (e.g., brainstem space-occupying lesions, Tourette syndrome, neuromyelitis optica spectrum disorder, cerebellar neurodegenerative diseases).[21]Al-Biltagi M, Bediwy AS, Saeed NK. Cough as a neurological sign: what a clinician should know. World J Crit Care Med. 2022 May 9;11(3):115-28.
https://www.wjgnet.com/2220-3141/full/v11/i3/115.htm
http://www.ncbi.nlm.nih.gov/pubmed/36331984?tool=bestpractice.com
In areas of endemic infection with fungi or parasites, diagnostic evaluation for these should be undertaken when more common causes of cough have been ruled out. Slow enlargement of intrathoracic blood vessels, such as an aortic aneurysm, may cause chronic cough.[22]Miller CP, Firoozan S, Woo EK, et al. Chronic cough: a herald symptom of thoracic aortic aneurysm in a patient with a bicuspid aortic valve. BMJ Case Rep. BMJ Case Rep. 2014 Sep 1;2014.
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4158188
http://www.ncbi.nlm.nih.gov/pubmed/25178892?tool=bestpractice.com
People who work with their voice (e.g., teachers, call center operators, actors, singers, coaches) may experience chronic cough and hoarseness.[16]Tarlo SM, Altman KW, Oppenheimer J, et al. Occupational and environmental contributions to chronic cough in adults: chest expert panel report. Chest. 2016 Oct;150(4):894-907.
http://www.ncbi.nlm.nih.gov/pubmed/27521735?tool=bestpractice.com
Coronavirus disease 2019 (COVID-19) may be associated with long-term symptoms, most commonly cough, low grade fever, and fatigue, and/or organ dysfunction.[23]Greenhalgh T, Knight M, A'Court C, et al. Management of post-acute covid-19 in primary care. BMJ. 2020 Aug 11;370:m3026.
https://www.doi.org/10.1136/bmj.m3026
http://www.ncbi.nlm.nih.gov/pubmed/32784198?tool=bestpractice.com
The definition and time frame of "postacute COVID-19 syndrome" or "long COVID" has not been universally determined. In the UK, "ongoing symptomatic COVID-19" has been defined as signs and symptoms of COVID-19 from 4-12 weeks. "Post-COVID-19 syndrome" is defined as signs and symptoms that develop during or after COVID-19 and continue for more than 12 weeks.[24]National Institute for Health and Care Excellence. COVID-19 rapid guideline: managing the long-term effects of COVID-19. Jan 2024 [internet publication].
https://www.nice.org.uk/guidance/ng188
Incidence, natural history, and etiology data continue to emerge. See Coronavirus disease 2019 (COVID-19).
Chronic cough that persists in spite of therapeutic trials and is otherwise unexplained by extensive evaluations is labeled as refractory chronic cough or unexplained chronic cough. In the literature, it is also referred to as neurogenic cough, cough hypersensitivity syndrome, or somatic cough.[25]Ahmad SR, Iyer VN. The evolving clinical practice of chronic cough. Mayo Clin Proc. 2022 Jun;97(6):1164-75.
https://www.mayoclinicproceedings.org/article/S0025-6196(22)00105-7/fulltext
http://www.ncbi.nlm.nih.gov/pubmed/35483988?tool=bestpractice.com
[26]Chung KF, McGarvey L, Song WJ, et al. Cough hypersensitivity and chronic cough. Nat Rev Dis Primers. 2022 Jun 30;8(1):45.
https://www.nature.com/articles/s41572-022-00370-w
http://www.ncbi.nlm.nih.gov/pubmed/35773287?tool=bestpractice.com