小结
定义
病史和体格检查
关键诊断因素
- 非对称听力受损
- 面部麻木
- 渐进式眩晕发作
其他诊断因素
- 耳鸣
- 声音定位困难
- 头痛
- 面部无力
- 眼泪增加或减少
- 金属味道或味觉减退
- 侧向凝视复视
- 眼球震颤
- 失去平衡和协调困难
- 眨眼变慢
- 吞咽困难
- 步态障碍
- 脑积水
- 视神经乳头水肿
- 颅内压升高
危险因素
- 神经纤维瘤病2 型
诊断性检查
首要检查
- 听力敏度图
- 头部钆增强 MRI
- 头颅 CT
- 听觉脑干反应
治疗流程
肿瘤<1~1.5 cm
肿瘤 1.5~3 cm
肿瘤 >3 cm
撰稿人
作者
Ryojo Akagami, BSc, MHsc, MD, FRCS(C), FAANS
Clinical Professor
University of British Columbia
Vancouver Health Sciences Centre
Division of Neurosurgery
Vancouver
British Columbia
Canada
利益声明
RA has been reimbursed for instructing at a dissection course by Stryker and gives yearly lectures at a Canadian resident review course. RA was an expert panelist at a session on vestibular schwannomas at the 2019 NASB meeting.
同行评议者
David Rowed, MD
Division of Neurosurgery
University of Toronto
Toronto
Ontario
Canada
利益声明
DR declares that he has no competing interests.
Laligam N. Sekhar, MD, FACS
Vice Chairman
Professor
Director
Cerebrovascular Surgery
Co-Director
Skull Base Surgery
Department of Neurological Surgery
University of Washington
Harborview Medical Center
Seattle
WA
利益声明
LNS declares that he has no competing interests.
Renn Holness, MD
Professor
Division of Neurosurgery
Dalhousie University
Halifax
Nova Scotia
Canada
利益声明
RH declares that she has no competing interests.
Iain Swan, MD, FRCS
Senior Lecturer in Otolaryngology
Honorary Consultant Otolaryngologist
Glasgow Royal Infirmary
Glasgow
UK
利益声明
IS declares that he has no competing interests.
Patrice Tran Ba Huy, MD
Department of Otorhinolaryngology-Head and Neck Surgery
AP-HP
Hopital Lariboisiere
Service ORL
Universite Paris 7
Paris and Laboratoire des Réseaux Sensorimoteurs
Paris
France
利益声明
PTBH declares that he has no competing interests.
鉴别诊断
- 脑膜瘤
- 表皮样
- 面神经雪旺细胞瘤
更多 鉴别诊断指南
- 前庭神经鞘瘤患者的管理指南
- 前庭神经鞘瘤患者的管理指南
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