小结
定义
病史和体格检查
关键诊断因素
- 腹泻
- 潮红
其他诊断因素
- 心悸
- 腹部绞痛
- 毛细血管扩张
- 右心衰的体征
- 心脏杂音
- 肝肿大
- 喘鸣
- 糙皮病
- 腹部肿块
危险因素
- 遗传性多发性内分泌肿瘤Ⅰ型(MEN-1)综合征
诊断性检查
首要检查
- 血清嗜铬粒蛋白A/B
- 尿 5-羟吲哚乙酸
- 生化检查
- 肝功能检查
- 全血细胞计数
需考虑的检查
- 胸部、腹部、骨盆和双相肝 CT
- 支气管镜检查
- 内镜检查
- 生长抑素受体显像 ± 生长抑素单光子发射 CT(SPECT)
- 碘(I)123 间碘苄胍(MIBG)核素显像
- 组织学
- PET 扫描
治疗流程
局限性疾病
转移性疾病
撰稿人
作者
Rajaventhan Srirajaskanthan, BSc (Hons), MD (Res), FRCP
Consultant Gastroenterologist
Neuroendocrine Tumour Unit
Kings College Hospital
London
UK
利益声明
RS has received research grants from AAA, Novartis and Ipsen, and has given consultancy advice to Pfizer and Ipsen. RS has engaged in the speaker's bureau for AAA, Ipsen, and Mylan.
Martyn Caplin, BSc, DM, FRCP
Professor
Consultant in Hepatobiliary and Gastroenterology
Neuroendocrine Tumour Unit
Royal Free Hospital
London
UK
利益声明
MC is on the advisory boards for Novartis, Ipsen, Lexicon, and Pfizer; he has also received speaker honoraria from them.
同行评议者
Wail Malaty, MD
Clinical Professor
Department of Family Medicine
University of North Carolina
Chapel Hill
Assistant Program Director
MAHEC Rural Family Medicine Residency
Hendersonville
NC
利益声明
WM declares that he has no competing interests.
Rajesh K. Garg, MD
Instructor in Medicine
Brigham and Women's Hospital
Division of Endocrinology
Diabetes and Hypertension
Boston
MA
利益声明
RKG declares that he has no competing interests.
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