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Síndrome da veia cava superior

Evidence last reviewed: 29 Mar 2026
Topic last updated: 18 Jul 2023

Summary

Definition

History and exam

Key diagnostic factors

  • presença de fatores de risco
  • edema localizado da face e dos membros superiores
  • dispneia
  • pletora facial
  • tosse
  • veias jugulares distendidas
  • veias torácicas distendidas
  • rouquidão
  • linfadenopatia
  • visão turva
  • estridor
  • confusão/letargia
Full details

Other diagnostic factors

  • anorexia
  • perda de peso
  • hemoptise
  • cefaleia
  • dor torácica
  • alterações mentais
  • febre
  • erupção cutânea
  • artralgia
  • edema laríngeo
  • cianose
  • papiledema
  • coma
Full details

Risk factors

  • tabagismo
  • múltiplos eletrodos de marca-passos
  • cateteres venosos centrais/porta
  • idade >50 anos
  • radiação
Full details

Diagnostic tests

1st tests to order

  • radiografia torácica
  • tomografia computadorizada (TC) do tórax
  • ressonância nuclear magnética (RNM) do tórax
  • ultrassonografia de membros superiores
Full details

Tests to consider

  • venografia
  • biópsia
  • citologia do escarro
  • toracocentese
  • cultura de escarro
  • velocidade de hemossedimentação
  • proteína C-reativa
Full details

Treatment algorithm

ACUTE

obstrução aguda das vias aéreas (sem diagnóstico tecidual)

ONGOING

etiologia maligna

etiologia infecciosa

etiologia iatrogênica

Contributors

Authors

Kul Aggarwal, MD, MRCP, FACC
Kul Aggarwal

Professor of Clinical Medicine

University of Missouri

Columbia

MO

Disclosures

KA declares that he has no competing interests.

Albert K. Chan, MD

Assistant Professor of Clinical Medicine

University of Missouri

Columbia

MO

Disclosures

AKC declares that he has no competing interests.

Acknowledgements

Professor Kul Aggarwal and Dr Albert K Chan would like to gratefully acknowledge Dr Nipun Arora and Lokesh Tejwani, previous contributors to this topic. NA declares that he has no competing interests.

Peer reviewers

Debabrata Mukherjee, MD

Gill Foundation Professor of Interventional Cardiology

Director of Cardiac Catheterization Laboratories

Gill Heart Institute

Division of Cardiovascular Medicine

University of Kentucky

Lexington

KY

Divulgaciones

DM declares that he has no competing interests.

Syed Wamique Yusuf, MD, MRCPI, FACC

Associate Professor

University of Texas MD Anderson Cancer Center

Department of Cardiology

Houston

TX

Divulgaciones

SWY declares that he has no competing interests.

Andrew Turley, MB ChB

Cardiology Specialist Registrar

The James Cook University Hospital

Middlesbrough

UK

Divulgaciones

AT declares that he has no competing interests.

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Referencias

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Artículos principales

Azizi AH, Shafi I, Shah N, et al. Superior vena cava syndrome. JACC Cardiovasc Interv. 2020 Dec 28;13(24):2896-2910.Texto completo  Resumen

American College of Radiology. ACR appropriateness criteria: suspected upper-extremity deep vein thrombosis. 2019 [internet publication].Texto completo

Uberoi R. Quality assurance guidelines for superior vena cava stenting in malignant disease. Cardiovasc Intervent Radiol. 2006 May-Jun;29(3):319-22. Resumen

​Kearon C, Akl EA, Ornelas J, et al. Antithrombotic therapy for VTE disease: CHEST guideline and expert panel report. Chest. 2016 Feb;149(2):315-52.Texto completo  Resumen

Artículos de referencia

Una lista completa de las fuentes a las que se hace referencia en este tema está disponible para los usuarios con acceso a todo BMJ Best Practice.
  • Síndrome da veia cava superior images
  • Diagnósticos diferenciais

    • Tamponamento cardíaco
    • Pericardite constritiva
    • Exacerbação aguda da doença pulmonar obstrutiva crônica (DPOC)
    Más Diferenciales
  • Diretrizes

    • ACR Appropriateness Criteria: suspected upper-extremity deep vein thrombosis
    • Antithrombotic therapy for VTE disease: CHEST guideline and expert panel report
    Más Diretrizes
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