Estenose pulmonar
Summary
Definition
病史和体格检查
关键诊断因素
- sopro sistólico de ejeção patológico com ou sem clique sistólico
其他诊断因素
- febre reumática
- dispneia
- fadiga
- dor torácica
- síncope
- características de dismorfismo da síndrome de Noonan
- características de dismorfismo na síndrome de Noonan com lentigos múltiplos
- características de dismorfismo da síndrome de Williams
- características de dismorfismo da síndrome de Alagille
- retardo do crescimento pôndero-estatural
- cianose
- sinais de insuficiência cardíaca direita
- ictus do ventrículo direito
- frêmito sistólico
危险因素
- etnia negra
- Síndrome de Noonan
- Síndrome de Noonan com lentigos múltiplos
- Síndrome de Alagille
- Síndrome de Williams
- síndrome da rubéola congênita
- síndrome carcinoide
- endocardite infecciosa
- tumores miocárdicos
- compressão externa
诊断性检查
首要检查
- eletrocardiograma (ECG)
- radiografia torácica
- ecocardiografia com avaliação por Doppler
需考虑的检查
- cateterismo cardíaco diagnóstico
- hemoglobina (Hb) e hematócrito (Hct)
- oximetria de pulso
- gasometria arterial
- ressonância nuclear magnética (RNM) cardíaca
- TC cardíaca
- teste ergométrico
治疗流程
doença leve
doença moderada
doença grave a crítica
撰稿人
作者
Jeremy Asnes, MD
Associate Professor of Pediatrics (Cardiology)
Yale Pediatric Cardiology
Yale New Haven Children's Hospital
New Haven
CT
利益声明
JA is a Principal Investigator for the Medtronic Harmony™ Transcatheter Pulmonary Valve clinical trial. JA has also been a paid consultant for Medtronic, the manufacturer of the Melody and Harmony transcatheter pulmonary valves.
Britton Keeshan, MD, MPH
Assistant Professor of Clinical Pediatrics
Yale Pediatric Cardiology
Yale New Haven Children's Hospital
New Haven
CT
利益声明
BK declares that he has no competing interests.
鸣谢
Dr Asnes and Dr Keeshan would like to gratefully acknowledge Dr Ivandito Kuntjoro, Dr Edgar Tay, Dr James Yip, Dr Kian Keong Pho, Dr Low Ting Ting, Dr Peter S. Fischbach, Dr Cyrus Samai, and Dr David M. Drossner, the previous authors of this topic.
利益声明
ET, IK, JY, KKP, LTT, PSF, CS and DD declared that they had no competing interests.
同行评议者
John Charpie, MD, PhD
Associate Professor of Pediatrics
Medical Director
Pediatric Cardiothoracic Intensive Care Unit
University of Michigan Congenital Heart Center
Ann Arbor
MI
利益声明
JC declares that he has no competing interests.
James Gnanapragasam, MBBS, MSc, FRCP, FRCPCH
Consultant in Paediatric Cardiology
Southampton University Hospitals NHS Trust
Southampton
UK
利益声明
JG declares that he has no competing interests.
Peer reviewer acknowledgements
BMJ Best Practice topics are updated on a rolling basis in line with developments in evidence and guidance. The peer reviewers listed here have reviewed the content at least once during the history of the topic.
Disclosures
Peer reviewer affiliations and disclosures pertain to the time of the review.
参考文献
关键文献
Stout KK, Daniels CJ, Aboulhosn JA, et al. 2018 AHA/ACC guideline for the management of adults with congenital heart disease: a report of the American College of Cardiology/American Heart Association Task Force on Clinical Practice Guidelines. J Am Coll Cardiol. 2018 Aug 10 [Epub ahead of print].全文 摘要
Otto CM, Nishimura RA, Bonow RO, et al. 2020 ACC/AHA guideline for the management of patients with valvular heart disease: executive summary: a report of the American College of Cardiology/American Heart Association Joint Committee on Clinical Practice Guidelines. Circulation. 2021 Feb 2;143(5):e35-71.全文 摘要
European Society of Cardiology. 2020 ESC guidelines for the management of adult congenital heart disease (previously grown-up congenital heart disease). Aug 2020 [internet publication].全文
参考文献
A full list of sources referenced in this topic is available to users with access to all of BMJ Best Practice.
鉴别诊断
- Sopro inocente
- Síndrome das costas retas
- Dilatação idiopática da artéria pulmonar
更多 鉴别诊断指南
- ACR appropriateness criteria: congenital or acquired heart disease
- Guidelines for cardiovascular intervention in adults with congenital heart disease
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Estenose pulmonar
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