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Fenômeno de Raynaud

Evidence last reviewed: 20 Apr 2026
Topic last updated: 04 Oct 2024

Summary

Definition

History and exam

Key diagnostic factors

  • presença de fatores de risco
  • dor ou desconforto nos dedos
  • parestesia digital
  • palidez dos dedos
  • descoloração vermelha e/ou azul dos dedos
  • capilares dilatados no leito ungueal
  • descoloração bem definida
  • ampliação dos leitos ungueais
Full details

Other diagnostic factors

  • pirose
  • disfagia
  • mãos inchadas
  • pele rígida
  • artralgia
  • fotossensibilidade
  • úlceras orais/nasais
  • alopécia
  • erupção cutânea em forma de borboleta
  • esclerodactilia
  • telangiectasia
  • dor torácica pleurítica
  • úlceras digitais
  • nódulos digitais
  • reabsorção dos tufos digitais
  • gangrena da ponta do dedo ou do dedo
  • lesões vermelhas dolorosas salientes nas pontas dos dedos
  • autoamputação
Full details

Risk factors

  • mulheres
  • história familiar
  • doença do tecido conjuntivo
  • uso de determinados medicamentos
  • lesão por vibração
  • Doença de Buerger
  • exposição prolongada ao frio/congelamento das extremidades
  • clima mais frio
  • tabagismo
  • isquemia
  • enxaqueca
  • glaucoma
Full details

Diagnostic tests

1st tests to order

  • diagnóstico clínico
  • fator antinuclear (FAN)
  • Hemograma completo
  • velocidade de hemossedimentação
  • proteína C-reativa
  • urinálise
Full details

Tests to consider

  • capilaroscopia
Full details

Treatment algorithm

ACUTE

fenômeno de Raynaud (FR) secundário grave: isquemia crítica, com úlceras digitais ou risco de perda de dedos

ONGOING

fenômeno de Raynaud (FR) primário ou secundário leve

Contributors

Authors

Janet Pope, MD, MPH, FRCPC
Janet Pope

Professor of Medicine

Division of Rheumatology

Department of Medicine

University of Western Ontario

Schulich School of Medicine and Dentistry

Head

Division of Rheumatology

St. Joseph's Health Care

London

Ontario

Canada

Disclosures

JP has been reimbursed for consulting with several pharmaceutical manufacturers unrelated to Rayaud’s phenomenon. JP’s institution receives research grants from BMS, Janssen, and Seattle Genetics. She has acted as a consultant for AbbVie, Amgen, AstraZeneca, BI, BMS, Celltrion, EMERALD, Frensenius Kabi, GSK, Janssen, JMP, Lilly, Mallinckrodt Pharmaceuticals, Mitsubishi Tanabe Pharma, Novartis, Organon, Pfizer, Sandoz, Samsung, and Viatris. JP is a speaker and advisory board member for AbbVie, Amgen, AstraZeneca, BI, BMS, Frensenius Kabi, GSK, Janssen, JMP, Lilly, Novartis, Organon, Pfizer, Sandoz, UCB, and Viatris. She receives no patents or royalties. JP is an author of a number of references cited in this topic.

Revisores por pares

Elena Schiopu, MD

Professor of Medicine

Rheumatologist

Medical College of Georgia at Augusta University

Charlie Norwood Veterans Affairs Medical Center

Augusta

GA

Divulgaciones

ES declares that she has no competing interests.

Ariane L. Herrick, MD FRCP

Reader in Rheumatology and Consultant Rheumatologist

Musculoskeletal Research Group

University of Manchester

Manchester

UK

Divulgaciones

ALH has been a paid speaker for Actelion; a consultant for Actelion and Pfizer; and an investigator in studies sponsored by Actelion, Mediquest, and United Therapeutics. ALH is an author of a number of references cited in this topic.

Bridget Griffiths, MB ChB, MD, MRCP(UK)

Consultant Rheumatologist

Department of Rheumatology

Freeman Hospital

Newcastle upon Tyne

UK

Divulgaciones

BG declares that she has no competing interests.

Agradecimiento de los revisores por pares

Los temas de BMJ Best Practice se actualizan de forma continua de acuerdo con los desarrollos en la evidencia y en las guías. Los revisores por pares listados aquí han revisado el contenido al menos una vez durante la historia del tema.

Divulgaciones

Las afiliaciones y divulgaciones de los revisores por pares se refieren al momento de la revisión.

Referencias

Nuestros equipos internos de evidencia y editoriales colaboran con colaboradores expertos internacionales y revisores pares para garantizar que brindemos acceso a la información más clínicamente relevante posible.

Artículos principales

Curtiss P, Svigos K, Schwager Z, et al. Part I: epidemiology, pathophysiology, and clinical considerations of primary and secondary Raynaud's phenomenon. J Am Acad Dermatol. 2024 Feb;90(2):223-34. Resumen

Belch J, Carlizza A, Carpentier PH, et al. ESVM guidelines - the diagnosis and management of Raynaud's phenomenon. Vasa. 2017 Oct;46(6):413-23.Texto completo  Resumen

Kowal-Bielecka O, Fransen J, Avouac J, et al. Update of EULAR recommendations for the treatment of systemic sclerosis. Ann Rheum Dis. 2017 Aug;76(8):1327-39.Texto completo  Resumen

Artículos de referencia

Una lista completa de las fuentes a las que se hace referencia en este tema está disponible para los usuarios con acceso a todo BMJ Best Practice.
  • Fenômeno de Raynaud images
  • Differentials

    • Resposta normal ao frio
    • Cianose/crioglobulinemia
    • Frieira (perniose)
    More Differentials
  • Guidelines

    • The 2024 British Society for Rheumatology guideline for management of systemic sclerosis
    • EULAR recommendations for the non-pharmacological management of systemic lupus erythematosus and systemic sclerosis
    More Guidelines
  • Patient information

    Fenômeno de Raynaud

    More Patient information
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