小结
定义
História e exame físico
Principais fatores diagnósticos
- systolic ejection murmur
- fixed splitting of the second heart sound
Outros fatores diagnósticos
- mid-diastolic murmur
- congestive cardiac failure
- faltering growth
- symptoms of atrial arrhythmias
- cyanosis
- finger clubbing
Fatores de risco
- female sex
- maternal alcohol consumption
- positive family history
Investigações diagnósticas
Primeiras investigações a serem solicitadas
- echocardiogram
- ECG
- chest x-ray
Investigações a serem consideradas
- pulse oximetry
- chest CT/MRI
- cardiac catheterization
Algoritmo de tratamento
pulmonary vascular resistance (PVR) <5 Wood units (WU) and Qp:Qs <1.5
PVR <5 WU and Qp:Qs ≥1.5, or evidence of right atrial enlargement
PVR ≥5 WU
Colaboradores
Autores
Christoph Haller, MD
Staff Cardiovascular Surgeon
Division of Cardiovascular Surgery
Labatt Family Heart Centre
The Hospital for Sick Children
Assistant Professor
University of Toronto
Toronto
Canada
Declarações
CH declares that he has no competing interests.
Agradecimentos
Dr Christoph Haller would like to gratefully acknowledge Dr Sachin Khambadkone, Dr Brandon Lane Phillips, Dr Frank Cetta, and Dr David J. Driscoll, previous contributors of this topic.
Declarações
SK, BLP, FC, and DJD declare that they have no competing interests.
Revisores
Chawki Elzein, MD
Professor of Surgery
University of Illinois at Chicago
Advocate Children's Hospital
Chicago
IL
Declarações
CE declares that he has no competing interests.
Peer reviewer acknowledgements
BMJ Best Practice topics are updated on a rolling basis in line with developments in evidence and guidance. The peer reviewers listed here have reviewed the content at least once during the history of the topic.
Disclosures
Peer reviewer affiliations and disclosures pertain to the time of the review.
Referências
Principais artigos
Jone PN, Ivy DD, Hauck A, et al. Pulmonary hypertension in congenital heart disease: a scientific statement from the American Heart Association. Circ Heart Fail. 2023 Jul;16(7):e00080.Texto completo Resumo
Baumgartner H, De Backer J, Babu-Narayan SV, et al; ESC Scientific Document Group. 2020 ESC guidelines for the management of adult congenital heart disease. Eur Heart J. 2021 Feb 11;42(6):563-645.Texto completo Resumo
Stout KK, Daniels CJ, Aboulhosn JA, et al. 2018 AHA/ACC guideline for the management of adults with congenital heart disease: a report of the American College of Cardiology/American Heart Association Task Force on clinical practice guidelines. Circulation. 2019 Apr 2;139(14):e698-800.Texto completo Resumo
Abrahamyan L, Dharma C, Alnasser S, et al. Long-term outcomes after atrial septal defect transcatheter closure by age and against population controls. JACC Cardiovasc Interv. 2021 Mar 8;14(5):566-75.Texto completo Resumo
Artigos de referência
Uma lista completa das fontes referenciadas neste tópico está disponível para os usuários com acesso total ao BMJ Best Practice.
Diagnósticos diferenciais
- Partial anomalous pulmonary venous drainage
- Ventricular septal defect
- Patent ductus arteriosus
Mais Diagnósticos diferenciaisDiretrizes
- ACR Appropriateness Criteria® congenital or acquired heart disease
- 2023 ESC guidelines for the management of infective endocarditis
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