Biliary atresia

References

Key articles

Bezerra JA, Wells RG, Mack CL, et al. Biliary Atresia: Clinical and Research Challenges for the Twenty-First Century. Hepatology. 2018 Sep;68(3):1163-1173.Full text  Abstract

Shneider BL, Brown MB, Haber B, et al. A multicenter study of the outcome of biliary atresia in the United States, 1997 to 2000. J Pediatr. 2006;148:467-474. Abstract

Reference articles

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17. Bezerra JA, Wells RG, Mack CL, et al. Biliary Atresia: Clinical and Research Challenges for the Twenty-First Century. Hepatology. 2018 Sep;68(3):1163-1173.Full text  Abstract

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19. Morecki R, Glaser JH, Cho S, et al. Biliary atresia and reovirus type 3 infection. N Engl J Med. 1982;307:481-484. Abstract

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25. Rosenberg DP, Morecki R, Lollini LO, et al. Extrahepatic biliary atresia in a rhesus monkey (Macaca mulatta). Hepatology. 1983;3:577-580. Abstract

26. Tyler KL, Sokol RJ, Oberhaus SM, et al. Detection of reovirus RNA in hepatobiliary tissues from patients with extrahepatic biliary atresia and choledochal cysts. Hepatology. 1998;27:1475-1482.Full text  Abstract

27. Steele MI, Marshall CM, Lloyd RE, et al. Reovirus 3 not detected by reverse transcriptase-mediated polymerase chain reaction analysis of preserved tissue from infants with cholestatic liver disease. Hepatology. 1995;21:697-702. Abstract

28. Lorent K, Gong W, Koo KA, et al. Identification of a plant isoflavonoid that causes biliary atresia. Sci Transl Med. 2015;7:286ra67.Full text  Abstract

29. Waisbourd-Zinman O, Koh H, Tsai S, et al. The toxin biliatresone causes mouse extrahepatic cholangiocyte damage and fibrosis through decreased glutathione and SOX17. Hepatology. 2016 Sep;64(3):880-93.Full text  Abstract

30. Zhao X, Lorent K, Wilkins BJ, et al. Glutathione antioxidant pathway activity and reserve determine toxicity and specificity of the biliary toxin biliatresone in zebrafish. Hepatology. 2016 Sep;64(3):894-907.Full text  Abstract

31. Silveira TR, Salzano FM, Donaldson PT, et al. Association between HLA and extrahepatic biliary atresia. J Pediatr Gastroenterol Nutr. 1993;16:114-117. Abstract

32. Kobayashi, H, Puri P, O'Briain DS, et al. Hepatic overexpression of MHC class II antigens and macrophage associated antigens (CD68) in patients with biliary atresia of poor prognosis. J Pediatr Surg. 1997;32:590-593. Abstract

33. Hart MH, Kaufman SS, Vanderhoof JA, et al. Neonatal hepatitis and extrahepatic biliary atresia associated with cytomegalovirus infection in twins. Am J Dis Child. 1991;145:302-305. Abstract

34. Danesino C, Spadoni E, Buzzi A. Familial biliary atresia. Am J Med Genet. 1999;85:195. Abstract

35. Ando K, Miyano T, Fujimoto T, et al. Sibling occurrence of biliary atresia and biliary dilatation. J Pediatr Surg. 1996;31:1302-1304. Abstract

36. Cheng G, Tang CS, Wong EH, et al. Common genetic variants regulating ADD3 gene expression alter biliary atresia risk. J Hepatol. 2013;59:1285-1291. Abstract

37. Garcia-Barceló MM, Yeung MY, Miao XP, et al. Genome-wide association study identifies a susceptibility locus for biliary atresia on 10q24.2. Hum Mol Genet. 2010;19:2917-2925.Full text  Abstract

38. Chen Y, Gilbert MA, Grochowski CM, et al. A genome-wide association study identifies a susceptibility locus for biliary atresia on 2p16.1 within the gene EFEMP1. PLoS Genet. 2018 Aug;14(8):e1007532.Full text  Abstract

39. Ningappa M, So J, Glessner J, et al. The Role of ARF6 in Biliary Atresia. PLoS One. 2015;10(9):e0138381.Full text  Abstract

40. Berauer JP, Mezina AI, Okou DT, et al. Identification of Polycystic Kidney Disease 1 Like 1 Gene Variants in Children With Biliary Atresia Splenic Malformation Syndrome. Hepatology. 2019 Sep;70(3):899-910.Full text  Abstract

41. Pickett LK, Briggs HC. Biliary obstruction secondary to hepatic vascular ligation in fetal sheep. J Pediatr Surg. 1969;4:95-101. Abstract

42. Klippel CH. A new theory of biliary atresia. J Pediatr Surg. 1972;7:651-654. Abstract

43. Ho CW, Shioda K, Shirasaki K, et al. The pathogenesis of biliary atresia: a morphological study of the hepatobiliary system and the hepatic artery. J Pediatr Gastroenterol Nutr. 1993;16:53-60. Abstract

44. Mack CL. The pathogenesis of biliary atresia: evidence for a virus-induced autoimmune disease. Semin Liver Dis. 2007;27:233-242. Abstract

45. Bezerra JA, Tiao G, Ryckman FC, et al. Genetic induction of proinflammatory immunity in children with biliary atresia. Lancet. 2002;360:1653-1659. Abstract

46. Bezerra JA. The next challenge in pediatric cholestasis: deciphering the pathogenesis of biliary atresia. J Pediatr Gastroenterol Nutr. 2006;43(suppl 1):S23-S29. Abstract

47. Russo P, Rand EB, Haber BA. Diseases of the biliary tree in infancy and childhood. In: Russo P, Ruchelli ED, Piccoli DA, eds. Pathology of pediatric gastrointestinal and liver disease. New York, NY: Springer; 2004:203-236.

48. Silveira TR, Salzano FM, Howard ER, et al. Extrahepatic biliary atresia and twinning. Braz J Med Biol Res. 1991;24:67-71. Abstract

49. Chardot C, Carton M, Spire-Bendelac N, et al. Epidemiology of biliary atresia in France: a national study 1986-96. J Hepatol. 1999;31:1006-1013. Abstract

50. Noorulla F, Dedon R, Maisels MJ. Association of early direct bilirubin levels and biliary atresia among neonates. JAMA Netw Open. 2019 Oct 2;2(10):e1913321.Full text  Abstract

51. Fawaz R, Baumann U, Ekong U, et al. Guideline for the evaluation of cholestatic jaundice in infants: joint recommendations of the North American Society for Pediatric Gastroenterology, Hepatology and Nutrition and the European Society for Pediatric Gastroenterology, Hepatology, and Nutrition. J Pediatr Gastroenterol Nutr. 2017;64:154-68.Full text  Abstract

52. Park WH, Choi SO, Lee HJ, et al. A new diagnostic approach to biliary atresia with emphasis on the ultrasonographic triangular cord sign: comparison of ultrasonography, hepatobiliary scintigraphy, and liver needle biopsy in the evaluation of infantile cholestasis. J Paediatr Surg. 1997;32:1555-1559. Abstract

53. Moreira RK, Cabral R, Cowles RA, et al. Biliary atresia: a multidisciplinary approach to diagnosis and management. Arch Pathol Lab Med. 2012 Jul;136(7):746-60.Full text  Abstract

54. Humphrey TM, Stringer MD. Biliary atresia: US diagnosis. Radiology. 2007;244:845-851. Abstract

55. Azar G, Beneck D, Lane B, et al. Atypical morphologic presentation of biliary atresia and value of serial liver biopsies. J Pediatr Gastroenterol Nutr. 2002;34:212-215. Abstract

56. Zerbini MC, Gallucci SD, Maezono R, et al. Liver biopsy in neonatal cholestasis: a review on statistical grounds. Mod Pathol. 1997;10:793-799. Abstract

57. Lurie M, Elmalach I, Schuger L, et al. Liver findings in infantile cytomegalovirus infection: similarity to extrahepatic biliary obstruction. Histopathology. 1987;11:1171-1180. Abstract

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65. Iinuma Y, Narisawa R, Iwafuchi M, et al. The role of endoscopic retrograde cholangiopancreatography in infants with cholestasis. J Pediatr Surg. 2000;35:545-549. Abstract

66. Norton KI, Glass RB, Kogan D, et al. MR cholangiography in the evaluation of neonatal cholestasis: initial results. Radiology. 2002;222:687-691. Abstract

67. Chen SM, Chang MH, Du JC, et al. Screening for biliary atresia by infant stool color card in Taiwan. Pediatrics. 2006;117:1147-1154. Abstract

68. Maki T, Sumasaki R, Matsui A. Biliary atresia: recent findings. Mass screening for biliary atresia. Jpn J Pediatr Surg. 1999;31:242-246.

69. Mushtaq I, Logan S, Morris M, et al. Screening of newborn infants for cholestatic hepatobiliary disease with tandem mass spectrometry. BMJ. 1999;319:471-477.Full text  Abstract

70. Schreiber RA, Barker CC, Roberts EA, et al. Biliary atresia: the Canadian experience. J Pediatr. 2007;151:659-665. Abstract

71. Ohi R. Surgery for biliary atresia. Liver. 2001 Jun;21(3):175-82.Full text  Abstract

72. Shneider BL, Brown MB, Haber B, et al. A multicenter study of the outcome of biliary atresia in the United States, 1997 to 2000. J Pediatr. 2006;148:467-474. Abstract

73. Altman RP, Lilly JR, Greenfeld J, et al. A multivariable risk factor analysis of the portoenterostomy (Kasai) procedure for biliary atresia: twenty-five years of experience from two centers. Ann Surg. 1997;226:348-355.Full text  Abstract

74. National Institutes of Health. Consensus development conference statement: liver transplantation - June 20-23, 1983. Hepatology. 1984;4(1 suppl):107S-110S. Abstract

75. Barshes NR, Lee TC, Balkrishnan R, et al. Orthotopic liver transplantation for biliary atresia: the U.S. experience. Liver Transpl. 2005;11:1193-1200.Full text  Abstract

76. Tyraskis A, Parsons C, Davenport M. Glucocorticosteroids for infants with biliary atresia following Kasai portoenterostomy. Cochrane Database Syst Rev. 2018 May 14;5:CD008735.Full text  Abstract

77. Squires RH, Ng V, Romero R, et al. Evaluation of the pediatric patient for liver transplantation: 2014 practice guideline by the American Association for the Study of Liver Diseases, American Society of Transplantation and the North American Society for Pediatric Gastroenterology, Hepatology and Nutrition. Hepatology. 2014;60:362-398.Full text  Abstract

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