References
Key articles
Prusiner SB. Shattuck lecture: neurodegenerative diseases and prions. N Engl J Med. 2001 May 17;344(20):1516-26.Full text Abstract
Department of Health. Minimise transmission risk of CJD and vCJD in healthcare settings. August 2017. [internet publication].Full text
Bouzamondo-Bernstein E, Hopkins SD, Spilman P, et al. The neurodegeneration sequence in prion diseases: evidence from functional, morphological and ultrastructural studies of the GABAergic system. J Neuropathol Exp Neurol. 2004 Aug;63(8):882-99. Abstract
Vitali P, Maccagnano E, Caverzasi E, et al. Diffusion-weighted MRI hyperintensity patterns differentiate CJD from other rapid dementias. Neurology. 2011 May 17;76(20):1711-9. Abstract
Josephson SA, Papanastassiou AM, Berger MS, et al. The diagnostic utility of brain biopsy procedures in patients with rapidly deteriorating neurological conditions or dementia. J Neurosurg. 2007 Jan;106(1):72-5.Full text Abstract
Vernino S, Geschwind MD, Boeve B. Autoimmune encephalopathies. Neurologist. 2007 May;13(3):140-7. Abstract
Geschwind MD, Haman A, Miller BL. Rapidly progressive dementia. Neurol Clin. 2007 Aug;25(3):783-807, vii. Abstract
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