Budd-Chiari syndrome

References

Key articles

Valla DC. The diagnosis and management of the Budd-Chiari syndrome: consensus and controversies. Hepatology. 2003;38:793-803. Abstract

Menon KV, Shah V, Kamath PS. The Budd-Chiari syndrome. N Engl J Med. 2004;350:578-585. Abstract

Socie G, Mary JY, de Gramont A, et al. Paroxysmal nocturnal haemoglobinuria: long term follow-up and prognostic factors. Lancet. 1996;348:573-577. Abstract

Perelló A, García-Pagán JC, Gilabert R, et al. TIPS is a useful long-term derivative therapy for patients with Budd-Chiari syndrome uncontrolled by medical therapy. Hepatology. 2002;35:132-139.Full text  Abstract

Reference articles

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27. Cazals-Hatem D, Vilgrain V, Genin P, et al. Arterial and portal circulation and parenchymal changes in Budd-Chiari syndrome: a study in 17 explanted livers. Hepatology. 2003;37:510-519.Full text  Abstract

28. McCuskey RS. Morphological mechanisms for regulating blood flow through hepatic sinusoids. Liver. 2000;20:3-7. Abstract

29. Murad SD, Plessier A, Hernandez-Guerra M, et al. A prospective follow-up study on 163 patients with Budd-Chiari syndrome: results from the European Network for Vascular Disorders of the Liver (EN-VIE). J Hepatol. 2007;46(Suppl 1):S4.Full text

30. Ohta M, Hashizume M, Tomikawa M, et al. Analysis of hepatic vein waveform by Doppler ultrasonography in 100 patients with portal hypertension. Am J Gastroenterol. 1994;89:170-175. Abstract

31. Buckley O, O'Brien J, Snow A, et al. Imaging of Budd-Chiari syndrome. Eur Radiol. 2007;17:2071-2078. Abstract

32. Kamath PS. Budd-Chiari syndrome: radiologic findings. Liver Transpl. 2006;12(suppl 2):S21-S22. Abstract

33. Noone TC, Semelka RC, Siegelman ES, et al. Budd-Chiari syndrome: spectrum of appearances of acute, subacute, and chronic disease with magnetic resonance imaging. J Magn Reson Imaging. 2000;11:44-50. Abstract

34. Erden A. Budd-Chiari syndrome: a review of imaging findings. Eur J Radiol. 2007;61:44-56. Abstract

35. Janssen HL, Garcia-Pagan JC, Elias E, et al. Budd-Chiari syndrome: a review by an expert panel. J Hepatol. 2003;38:364-371.Full text  Abstract

36. Baxter EJ, Scott LM, Campbell PJ, et al. Acquired mutation of the tyrosine kinase JAK2 in human myeloproliferative disorders. Lancet. 2005 Mar 19-25;365(9464):1054-61. Abstract

37. Qi X, Yang Z, Bai M, et al. Meta-analysis: the significance of screening for JAK2V617F mutation in Budd-Chiari syndrome and portal venous system thrombosis. Aliment Pharmacol Ther. 2011;33:1087-1103. Abstract

38. Brière JB. Budd-Chiari syndrome and portal vein thrombosis associated with myeloproliferative disorders: diagnosis and management. Semin Thromb Hemost. 2006;32:208-218. Abstract

39. Menon KV, Shah V, Kamath PS. The Budd-Chiari syndrome. N Engl J Med. 2004;350:578-585. Abstract

40. Tang TJ, Batts KP, de Groen PC, et al. The prognostic value of histology in the assessment of patients with Budd-Chiari syndrome. J Hepatol. 2001;35:338-343. Abstract

41. Hall SE, Rosse WF. The use of monoclonal antibodies and flow cytometry in the diagnosis of paroxysmal nocturnal hemoglobinuria. Blood. 1996;87:5332-5340.Full text  Abstract

42. Tanaka M, Wanless IR. Pathology of the liver in Budd-Chiari syndrome: portal vein thrombosis and the histogenesis of veno-centric cirrhosis, veno-portal cirrhosis, and large regenerative nodules. Hepatology. 1998;27:488-496.Full text  Abstract

43. DeLeve LD, Shulman HM, McDonald GB. Toxic injury to hepatic sinusoids: sinusoidal obstruction syndrome (veno-occlusive disease). Semin Liver Dis. 2002;22:27-42. Abstract

44. Salat C, Holler E, Kolb HJ, et al. Plasminogen activator inhibitor-1 confirms the diagnosis of hepatic veno-occlusive disease in patients with hyperbilirubinemia after bone marrow transplantation. Blood. 1997;89:2184-2188.Full text  Abstract

45. Yoshimoto K, Ono N, Okamura T, et al. Recent progress in the diagnosis and therapy for veno-occlusive disease of the liver. Leuk Lymphoma. 2003;44:229-234. Abstract

46. Shulman HM, McDonald GB, Matthews D, et al. An analysis of hepatic venocclusive disease and centrilobular hepatic degeneration following bone marrow transplantation. Gastroenterology. 1980;79:1178-1191. Abstract

47. Bargalló X, Gilabert R, Nicolau C, et al. Sonography of Budd-Chiari syndrome. Am J Roentgenol. 2006;187:W33-W41.Full text  Abstract

48. Frank JW, Kamath PS, Stanson AW. Budd-Chiari syndrome: early intervention with angioplasty and thrombolytic therapy. Mayo Clin Proc. 1994;69:877-881. Abstract

49. Plessier A, Sibert A, Consigny Y, et al. Aiming at minimal invasiveness as a therapeutic strategy for Budd-Chiari syndrome. Hepatology. 2006;44:1308-1316.Full text  Abstract

50. De Franchis R. Evolving consensus in portal hypertension: report of the Baveno IV Consensus Workshop on methodology of diagnosis and therapy in portal hypertension. J Hepatol. 2005;43:167-176.Full text  Abstract

51. Sholar PW, Bell WR. Thrombolytic therapy for inferior vena cava thrombosis in paroxysmal nocturnal hemoglobinuria. Ann Intern Med. 1985;103:539-541. Abstract

52. Alioglu B, Avci Z, Aytekin C, et al. Budd-Chiari syndrome in a child due to a membranous web of the inferior vena cava resolved by systemic and local recombinant tissue plasminogen activator treatment. Blood Coagul Fibrinolysis. 2006;17:209-212. Abstract

53. Hillmen P, Muus P, Dührsen U, et al. Effect of the complement inhibitor eculizumab on thromboembolism in patients with paroxysmal nocturnal hemoglobinuria. Blood. 2007;110:4123-4128.Full text  Abstract

54. Rhee J, Demetris AJ, Abu Elmagd K, et al. Suprahepatic Budd-Chiari syndrome treated with thrombectomy and cavoplasty. Dig Dis Sci. 2003;48:1637-1641. Abstract

55. Yang XL, Cheng TO, Chen CR. Successful treatment by percutaneous balloon angioplasty of Budd-Chiari syndrome caused by membranous obstruction of inferior vena cava: 8-year follow-up study. J Am Coll Cardiol. 1996;28:1720-1724. Abstract

56. Cooper S, Olliff S, Elias E. Recanalisation of hepatic veins by a combined transhepatic, transjugular approach in three cases of Budd Chiari syndrome. J Interv Radiol. 1996;11:9-13.

57. Eapen CE, Velissaris D, Heydtmann M, et al. Favourable medium term outcome following hepatic vein recanalisation and/or transjugular intrahepatic portosystemic shunt for Budd Chiari syndrome. Gut. 2006 Jun;55(6):878-84.Full text  Abstract

58. Pelage JP, Denys A, Valla D, et al. Budd-Chiari syndrome due to prothrombotic disorder: mid-term patency and efficacy of endovascular stents. Eur Radiol. 2003;13:286-293. Abstract

59. Rogopoulos A, Gavelli A, Sakai H, et al. Transjugular intrahepatic portosystemic shunt for Budd-Chiari syndrome after failure of surgical shunting. Arch Surg. 1995;130:227-228. Abstract

60. Beckett D, Olliff S. Interventional radiology in the management of Budd Chiari syndrome. Cardiovasc Intervent Radiol. 2008;31:839-847. Abstract

61. Lee BB, Villavicencio L, Kim YW, et al. Primary Budd-Chiari syndrome: outcome of endovascular management for suprahepatic venous obstruction. J Vasc Surg. 2006;43:101-108. Abstract

62. Wu T, Wang L, Xiao Q, et al. Percutaneous balloon angioplasty of inferior vena cava in Budd-Chiari syndrome-R1. Int J Cardiol. 2002;83:175-178. Abstract

63. LaBerge JM, Ring EJ, Lake JR, et al. Transjugular intrahepatic portosystemic shunts: preliminary results in 25 patients. J Vasc Surg. 1992;16:258-267. Abstract

64. Ochs A, Sellinger M, Haag K, et al. Transjugular intrahepatic portosystemic stent-shunt (TIPS) in the treatment of Budd-Chiari syndrome. J Hepatol. 1993;18:217-225. Abstract

65. Watanabe H, Shinzawa H, Saito T, et al. Successful emergency treatment with a transjugular intrahepatic portosystemic shunt for life-threatening Budd-Chiari syndrome with portal thrombotic obstruction. Hepatogastroenterology. 2000;47:839-841. Abstract

66. Ganger DR, Klapman JB, McDonald V, et al. Transjugular intrahepatic portosystemic shunt (TIPS) for Budd-Chiari syndrome or portal vein thrombosis: review of indications and problems. Am J Gastroenterol. 1999;94:603-608. Abstract

67. Hernandez-Guerra M, Turnes J, Rubinstein P, et al. PTFE-covered stents improve TIPS patency in Budd-Chiari syndrome. Hepatology. 2004;40:1197-1202.Full text  Abstract

68. Wang ZG, Jones RS. Budd-Chiari syndrome. Curr Probl Surg. 1996;33:83-211. Abstract

69. Senning A. Transcaval posterocranial resection of the liver as treatment of the Budd-Chiari syndrome. World J Surg. 1983;7:632-640. Abstract

70. Ringe B, Lang H, Oldhafer KJ, et al. Which is the best surgery for Budd-Chiari syndrome: venous decompression or liver transplantation? A single-center experience with 50 patients. Hepatology. 1995;21:1337-1344. Abstract

71. Ara C, Akbulut S, Ince V, et al. Living donor liver transplantation for Budd-Chiari syndrome: Overcoming a troublesome situation. Medicine (Baltimore). 2016 Oct;95(43):e5136.Full text  Abstract

72. Yamada T, Tanaka K, Ogura Y, et al. Surgical techniques and long-term outcomes of living donor liver transplantation for Budd-Chiari syndrome. Am J Transplant. 2006;6:2463-2469. Abstract

73. Zhang Q, Xu H, Zu M, et al. Catheter-directed thrombolytic therapy combined with angioplasty for hepatic vein obstruction in Budd-Chiari syndrome complicated by thrombosis. Exp Ther Med. 2013 Oct;6(4):1015-1021.Full text  Abstract

74. Bismuth H, Sherlock DJ. Portasystemic shunting versus liver transplantation for the Budd Chiari syndrome. Ann Surg. 1991;214:581-589.Full text  Abstract

75. Mahmoud AE, Elias E, Beauchamp N, et al. Prevalence of the factor V Leiden mutation in hepatic and portal vein thrombosis. Gut. 1997;40:798-800.Full text  Abstract

76. Darwish Murad S, Valla DC, de Groen PC, et al. Pathogenesis and treatment of Budd-Chiari syndrome combined with portal vein thrombosis. Am J Gastroenterol. 2006;101:83-90. Abstract

77. Hillmen P, Lewis SM, Bessler M, et al. Natural history of paroxysmal nocturnal haemoglobinuria. New Engl J Med. 1995;333:1253-1259.Full text  Abstract

78. Socie G, Mary JY, de Gramont A, et al. Paroxysmal nocturnal haemoglobinuria: long term follow-up and prognostic factors. Lancet. 1996;348:573-577. Abstract

79. McCarthy PM, van Heerden JA, Adson MA, et al. The Budd-Chiari syndrome: medical and surgical management of 30 patients. Arch Surg. 1985;120:657-662. Abstract

80. Ahn SS, Yellin A, Sheng FC, et al. Selective surgical therapy of the Budd-Chiari syndrome provides superior survivor rates than conservative medical management. J Vasc Surg. 1987;5:28-37. Abstract

81. Zhang CQ, Fu LN, Xu L, et al. Long-term effect of stent placement in 115 patients with Budd-Chiari syndrome. World J Gastroenterol. 2003;9:2587-2591.Full text  Abstract

82. Garcia-Pagán JC, Heydtmann M, Raffa S, et al. TIPS for Budd-Chiari syndrome: long-term results and prognostics factors in 124 patients. Gastroenterology. 2008;135:808-815. Abstract

83. Perelló A, García-Pagán JC, Gilabert R, et al. TIPS is a useful long-term derivative therapy for patients with Budd-Chiari syndrome uncontrolled by medical therapy. Hepatology. 2002;35:132-139.Full text  Abstract

84. Schattenfroh N, Bechstein WO, Blumhardt G, et al. Liver transplantation for PNH with Budd-Chiari syndrome: a case report. Transpl Int. 1993;6:354-358. Abstract

85. Slakey DP, Klein AS, Venbrux AC, et al. Budd-Chiari syndrome: current management options. Ann Surg. 2001;233:522-527.Full text  Abstract

86. Mentha G, Giostra E, Majno PE, et al. Liver transplantation for Budd-Chiari syndrome: a European study on 248 patients from 51 centres. J Hepatol. 2006;44:520-528. Abstract

87. Knoop M, Lemmens HP, Langrehr JM, et al. Liver transplantation for Budd-Chiari syndrome. Transplant Proc. 1994;26:3577-3578. Abstract

88. Smalberg JH, Darwish Murad S, Braakman E, et al. Myeloproliferative disease in the pathogenesis and survival of Budd-Chiari syndrome. Haematologica. 2006;91:1712-1713.Full text  Abstract

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90. Holland-Fischer P, Gronbaek H, Astrup L, et al. Budd-Chiari and inferior caval vein syndromes due to membranous obstruction of liver veins: successful treatment with angioplasty and transcaval transjugular intrahepatic porto-systemic shunt. Scand J Gastroenterol. 2004;39:1025-1028. Abstract

91. Ren W, Qi X, Yang Z, et al. Prevalence and risk factors of hepatocellular carcinoma in Budd-Chiari syndrome: a systematic review. Eur J Gastroenterol Hepatol. 2013 Jul;25(7):830-41. Abstract

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