The UK incidence rate of CTCL was 0.4 per 100,000 per year in 2003.Data from the US suggest an age-adjusted incidence of 0.64 per 100,000. However, as most are low-grade malignancies with long-term survival, the overall prevalence is much higher. Approximately two-thirds of primary cutaneous lymphomas are of T-cell origin, of which the majority are mycosis fungoides (MF). MF represents <3% of the non-Hodgkin's lymphomas. Studies have suggested that the incidence is rising, but this may in fact be due to improved diagnosis and better registration. In the UK and US, MF is more common in older people and men; data from the US suggest MF is more common in black Americans. Age-adjusted incidence, relative to white people, is 1.7 for black Americans and 0.6 for Asians. However, Sézary's syndrome appears to have a higher incidence among white Americans.
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