Last reviewed: November 2017
Last updated: November  2017

Summary

Definition

History and exam

Key diagnostic factors

  • hypertension presenting at a young age or resistant to treatment
  • diminished lower extremity pulses
  • differential upper and lower extremity BPs

Other diagnostic factors

  • systolic ejection murmur
  • male gender
  • genetic syndrome
  • claudication
  • headache
  • systolic ejection click
  • other cardiac anomalies

Risk factors

  • male gender
  • young age
  • FHx
  • Turner's syndrome
  • DiGeorge's syndrome
  • hypoplastic left heart syndrome
  • Shone's complex
  • PHACE syndrome

Diagnostic investigations

1st investigations to order

  • ECG
  • CXR
  • echocardiogram
Full details

Investigations to consider

  • CT angiography
  • magnetic resonance angiography
  • cardiac catheterisation
Full details

Treatment algorithm

Contributors

Authors VIEW ALL

Jeffrey Gossett

Director Heart Failure, Heart Transplantation

Professor of Pediatrics

Division of Pediatric Cardiology

University of California, San Francisco

San Francisco

CA

Disclosures

JG declares that he has no competing interests.

Anna Kamp

Assistant Professor

Pediatric Cardiology

University of Kentucky

Lexington

KY

Disclosures

AK declares that she has no competing interests.

Peer reviewers VIEW ALL

Clinical Assistant Professor of Pediatrics

University of Michigan

Ann Arbor

MI

Disclosures

RA declares that he has no competing interests.

Consultant Paediatric Cardiologist and Honorary Senior Lecturer

Great Ormond Street Hospital and Institute of Child Health

London

UK

Disclosures

SK declares that he has no competing interests.

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