Summary
- Rare systemic small-vessel vasculitis associated with asthma and eosinophilia.
- Classic pathological triad of tissue eosinophilia, granulomatous inflammation, and vasculitis.
- Associated with perinuclear anti-neutrophil cytoplasmic antibody (p-ANCA), the target antigen of which is myeloperoxidase (MPO).
- The cornerstone of treatment is corticosteroids. Severe disease is treated in a similar manner to other ANCA-associated vasculitides, with additional immunosuppressive agents.
- Cardiac involvement causes significant morbidity and mortality.
Other related conditions
- Asthma in adults
- Systemic vasculitis
- Granulomatosis with polyangiitis (Wegener's)
- Allergic bronchopulmonary aspergillosis
- Allergic rhinitis
- Assessment of eosinophilia
- Bladder cancer
- Chronic sinusitis
- Cryoglobulinaemia
- Giant cell arteritis
- Henoch-Schonlein purpura
- Infertility in women
- Kawasaki disease
- Male factor infertility
- Osteoporosis
- Overview of pneumonia
- Polyarteritis nodosa
- Takayasu's arteritis
Last updated: Jan 02, 2013
