- Autosomal-recessive condition characterised by a predominantly conjugated hyperbilirubinaemia.
- Patients are generally asymptomatic and jaundice may be an incidental finding.
- Over 50% of the serum bilirubin is conjugated and bilirubinuria is typically present.
- Symptomatically similar to Dubin-Johnson syndrome but the liver is histologically normal.
- A benign condition with a normal life expectancy, and no specific therapy is required.
last updated:=최종 업데이트: 4월 05, 2013