Zusammenfassung
- An inflammatory disorder involving both the peripheral bronchioles and alveoli simultaneously. It has distinctive radiographic findings, histological features, and response to corticosteroids (unlike usual interstitial pneumonia).
- Most common type is idiopathic BOOP; other types include focal nodular, post-infection, drug-related, rheumatological, immunological, organ transplantation, radiotherapy, environmental, and miscellaneous BOOP.
- Accounts for 20% to 30% of all cases of chronic infiltrative lung diseases. It occurs equally among men and women, and is not related to smoking.
- High-resolution chest CT scan shows bilateral patchy triangular ground glass opacities with air bronchograms usually located peripherally.
- Lung biopsy may be required to establish the definitive diagnosis in patients with unusual findings or severe disease.
- Idiopathic BOOP is treated with corticosteroids.
- Cases with an underlying cause (e.g., drug-related BOOP) should have the causative factor removed; corticosteroid therapy is indicated in some cases.
Other related conditions
- Antiphospholipid syndrome
- Cirrhosis
- Cryptococcosis
- Interstitial cystitis
- Malaria infection
- Pneumocystis jirovecii pneumonia
- Pulmonary tuberculosis
- Sarcoidosis
- Granulomatosis with polyangiitis (Wegener's)
- Rheumatoid arthritis
- Systemic lupus erythematosus
- Systemic sclerosis (scleroderma)
- Dermatomyositis
- Ankylosing spondylitis
- Behcet's syndrome
- Sjogren's syndrome
- Polymyalgia rheumatica
- Community-acquired pneumonia
- Hospital-acquired pneumonia
- Aspiration pneumonia
- Acute respiratory distress syndrome
- Hypersensitivity pneumonitis
- Bronchiolitis
- Crohn's disease
- Ulcerative colitis
- HIV infection
- Cocaine abuse
- Myelodysplastic syndrome
- Primary biliary cirrhosis
- Cryoglobulinaemia
Letzte Aktualisierung am: Mai 21, 2013
